A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation

نویسندگان

  • Sanaa Hammi
  • Hajar Berrani
  • Thami Benouchen
  • Naima Lamlami
  • Imane Elkhiyat
  • Jamal Eddine Bourkadi
چکیده

Primary intestinal lymphangiectasia (Waldmann's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically.

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عنوان ژورنال:

دوره 26  شماره 

صفحات  -

تاریخ انتشار 2017